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Composition and Function of Decellularized Human Lung Extracellular Matrix from Congenital Pulmonary Airway Malformation

Yanan Li, Ping Yang, Miao Yuan, Xinglong Zhu, Shengqiang Mao, Ying Yang, Menglin Yao, Fei Chen, Yanyan Zhou, Ji Bao, Chang Xu, Yi Li

Journal of Clinical Medicine · 2026

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Background: Congenital pulmonary airway malformation (CPAM) is a rare developmental disorder characterized by cystic lung lesions, yet its extracellular matrix (ECM) composition remains poorly understood. This study employed decellularization and data-independent acquisition (DIA) proteomics to compare ECM profiles between cystic (CPAM) and histologically normal non-diseased (ND) regions from the lungs of four patients. Results: The decellularized scaffolds retained their native architecture with minimal residual DNA (

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Autor:innen
Yanan Li, Ping Yang, Miao Yuan, Xinglong Zhu, Shengqiang Mao, Ying Yang, Menglin Yao, Fei Chen, Yanyan Zhou, Ji Bao, Chang Xu, Yi Li
Quelle
Journal of Clinical Medicine
Publikation
2026-01-01
Band / Ausgabe
Nicht angegeben
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Nicht angegeben
ISSN / ISBN
2077-0383
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Zitierfähiger Nachweis

Yanan Li, Ping Yang, Miao Yuan, Xinglong Zhu, Shengqiang Mao, Ying Yang, Menglin Yao, Fei Chen, Yanyan Zhou, Ji Bao, Chang Xu, Yi Li (2026). Composition and Function of Decellularized Human Lung Extracellular Matrix from Congenital Pulmonary Airway Malformation. Journal of Clinical Medicine. https://doi.org/10.3390/jcm15176742
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